{"id":30294,"date":"2019-08-25T23:24:13","date_gmt":"2019-08-25T21:24:13","guid":{"rendered":"https:\/\/progena.ch\/was-ist-duchenne\/"},"modified":"2020-03-08T21:40:33","modified_gmt":"2020-03-08T20:40:33","slug":"was-ist-duchenne","status":"publish","type":"page","link":"https:\/\/progena.ch\/fr\/was-ist-duchenne\/","title":{"rendered":"Duchenne, c\u2019est quoi?"},"content":{"rendered":"\n[et_pb_section fb_built=\u00a0\u00bb1&Prime; fullwidth=\u00a0\u00bbon\u00a0\u00bb admin_label=\u00a0\u00bbSection\u00a0\u00bb module_id=\u00a0\u00bbhome\u00a0\u00bb _builder_version=\u00a0\u00bb3.22&Prime; custom_padding=\u00a0\u00bb0px|0px|0px|0px\u00a0\u00bb transparent_background=\u00a0\u00bboff\u00a0\u00bb make_fullwidth=\u00a0\u00bboff\u00a0\u00bb use_custom_width=\u00a0\u00bboff\u00a0\u00bb width_unit=\u00a0\u00bboff\u00a0\u00bb custom_width_px=\u00a0\u00bb1080px\u00a0\u00bb custom_width_percent=\u00a0\u00bb80%\u00a0\u00bb fb_built=\u00a0\u00bb1&Prime; bb_built=\u00a0\u00bb1&Prime; _i=\u00a0\u00bb0&Prime; 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_builder_version=\u00a0\u00bb3.27.4&Prime; custom_padding=\u00a0\u00bb20px||||false|false\u00a0\u00bb fb_built=\u00a0\u00bb1&Prime; _i=\u00a0\u00bb1&Prime; _address=\u00a0\u00bb1&Prime;][et_pb_row column_structure=\u00a0\u00bb2_3,1_3&Prime; admin_label=\u00a0\u00bbLigne\u00a0\u00bb _builder_version=\u00a0\u00bb3.27.4&Prime; make_fullwidth=\u00a0\u00bboff\u00a0\u00bb use_custom_width=\u00a0\u00bboff\u00a0\u00bb width_unit=\u00a0\u00bboff\u00a0\u00bb custom_width_px=\u00a0\u00bb1080px\u00a0\u00bb custom_width_percent=\u00a0\u00bb80%\u00a0\u00bb _i=\u00a0\u00bb0&Prime; _address=\u00a0\u00bb1.0&Prime;][et_pb_column type=\u00a0\u00bb2_3&Prime; _builder_version=\u00a0\u00bb3.25&Prime; custom_padding=\u00a0\u00bb|||\u00a0\u00bb _i=\u00a0\u00bb0&Prime; _address=\u00a0\u00bb1.0.0&Prime; custom_padding__hover=\u00a0\u00bb|||\u00a0\u00bb][et_pb_text _builder_version=\u00a0\u00bb3.27.4&Prime; text_orientation=\u00a0\u00bbcenter\u00a0\u00bb hover_enabled=\u00a0\u00bb0&Prime; text_text_align=\u00a0\u00bbcenter\u00a0\u00bb _i=\u00a0\u00bb0&Prime; _address=\u00a0\u00bb1.0.0.0&Prime;]<h1> Duchenne, c\u2019est quoi? <\/h1>[\/et_pb_text][et_pb_text _builder_version=\u00a0\u00bb3.27.4&Prime; hover_enabled=\u00a0\u00bb0&Prime; _i=\u00a0\u00bb1&Prime; _address=\u00a0\u00bb1.0.0.1&Prime;]<p><strong>La dystrophie musculaire de Duchenne (DMD) et la dystrophie musculaire de Becker (BMD) sont des maladies musculaires rares.<\/strong><\/p>\n<p>Guillaume-Benjamin Duchenne a d\u00e9crit la dystrophie musculaire \u00e0 Paris au XIXe si\u00e8cle. La <strong>dystrophie musculaire de Duchenne<\/strong> touche presque exclusivement les gar\u00e7ons. Il survient \u00e0 une fr\u00e9quence d&rsquo;un gar\u00e7on nouveau-n\u00e9 sur 3500.<br \/> Selon le Registre suisse des patients, 205 personnes affect\u00e9es vivent en Suisse (2019). Chaque ann\u00e9e, environ 5 gar\u00e7ons atteints de DMD sont enregistr\u00e9s dans le registre suisse des patients.<\/p>\n<p><em>En savoir plus sur la dystrophie musculaire de Duchenne sur le <a href=\"https:\/\/www.afm-telethon.fr\/dystrophie-musculaire-duchenne-1251\" target=\"_blank\" rel=\"noopener noreferrer\">site de l\u2019AFM-Telethon<\/a>\u00a0<\/em><\/p>\n<p>La <strong>dystrophie musculaire de Becker<\/strong> (BMD) tire son nom du m\u00e9decin allemand Peter Emil Becker, qui a diagnostiqu\u00e9 les premiers patients dans les ann\u00e9es 50 et 60.<br \/> On ne sait pas combien de personnes touch\u00e9es vivent en Suisse. Presque seuls les gar\u00e7ons sont touch\u00e9s par la BMD, mais la maladie est 10 fois moins courante que la DMD. L&rsquo;incidence est de 1 naissance masculine sur 20 000.<\/p>\n<p><em>Pour en savoir plus sur la dystrophie musculaire de Becker, consultez le <a href=\"https:\/\/www.afm-telethon.fr\/dystrophie-musculaire-becker-1235\" target=\"_blank\" rel=\"noopener noreferrer\">site Internet de de l\u2019AFM-Telethon<\/a><\/em><\/p>\n<p>Cette vid\u00e9o de la fondation Belge Little O (littleo.eu) explique clairement la cause, le cours et les options de traitement de la dystrophie de Duchenne.<strong><\/strong><\/p>\n[\/et_pb_text][et_pb_video src=\u00a0\u00bbhttps:\/\/youtu.be\/TTLXAOL8k5Q\u00a0\u00bb _builder_version=\u00a0\u00bb3.27.4&Prime; hover_enabled=\u00a0\u00bb0&Prime; _i=\u00a0\u00bb2&Prime; _address=\u00a0\u00bb1.0.0.2&Prime;][\/et_pb_video][\/et_pb_column][et_pb_column type=\u00a0\u00bb1_3&Prime; _builder_version=\u00a0\u00bb3.25&Prime; custom_padding=\u00a0\u00bb|||\u00a0\u00bb _i=\u00a0\u00bb1&Prime; _address=\u00a0\u00bb1.0.1&Prime; custom_padding__hover=\u00a0\u00bb|||\u00a0\u00bb][et_pb_sidebar area=\u00a0\u00bbet_pb_widget_area_3&Prime; _builder_version=\u00a0\u00bb3.27.4&Prime; body_font=\u00a0\u00bb|||on|||||\u00a0\u00bb body_text_align=\u00a0\u00bbright\u00a0\u00bb body_font_size=\u00a0\u00bb14px\u00a0\u00bb body_letter_spacing=\u00a0\u00bb1px\u00a0\u00bb body_line_height=\u00a0\u00bb2em\u00a0\u00bb _i=\u00a0\u00bb0&Prime; _address=\u00a0\u00bb1.0.1.0&Prime;][\/et_pb_sidebar][\/et_pb_column][\/et_pb_row][\/et_pb_section]\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","footnotes":""},"class_list":["post-30294","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Duchenne, c\u2019est quoi? 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